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Elsevier, Paediatric Respiratory Reviews

DOI: 10.1016/j.prrv.2015.12.003

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Respiratory manifestations and management in children with Common Variable Immunodeficiency

Journal article published in 2016 by Chetan Pandit, Peter Hsu, Peter van Asperen, Sam Mehr ORCID
This paper is available in a repository.
This paper is available in a repository.

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Abstract

Common variable immunodeficiency is an antibody deficiency that usually presents in childhood with recurrent sino-pulmonary infections. Diagnostic delay is frequent and thus respiratory morbidity is common, ranging from recurrent suppurative bronchitis to bronchiectasis. Immunoglobulin replacement therapy is the mainstay of treatment, whilst prophylactic antibiotic therapy and muco-ciliary clearance are additional treatment options. This review examines the diagnosis and management of respiratory issues in children with CVID.