Tracheobronchopathia osteoplastica (TO) is a benign osseous metaplasia of the laryngotracheobronchial tree. TO is diagnosed more frequently in men over 50 years of age. Symptoms are non-specific, and include dry cough, sore throat, dyspnea, and hemoptysis. Here, we have reported a 49-year-old man who had TO and Behçet's disease (BD). He was admitted with chest pain and productive cough lasting for two weeks. However, his symptoms have been relapsing occasionally for two years. Therefore, we thought that his diagnosis could be BD with lung involvement. Physical examination was normal. There was upper respiratory airway obstruction in pulmonary function tests. Chest computerized tomography demonstrated multilple nodular densities along trachea and main carina. He underwent a fiberoptic bronchoscopic examination and we found multiple white nodules from proximal trachea to the main carina. Bronchoscopic appearance was typical for TO. Our case was interesting, because he had TO which was accompanied with BD.