Hair tourniquet syndrome is a rare medical condition involving a tightly constricting strand of hair or thread-like material strangulating a part of the bodily appendage, such as the fingers and toes, which prompts for urgent attention. Failure to recognize early and respond to worsening symptoms may lead to serious complications. Few cases have been reported as this condition affects primarily young children. Our aim for this topic is to increase awareness of hair tourniquet syndrome to healthcare providers. Proper exposure during routine physical examination for early detection, and timely referral for effective treatment. Here we report a case of hair tourniquet syndrome of the toe that was released surgically with a good outcome. Keywords: Hair tourniquet syndrome, bodily appendage, children.