Rhabdomyosarcoma is a highly aggressive malignant tumor with an incidence of 1/500,000 children per year. It originates from mesenchymal cell to invade soft tissue, developing into a highly aggressive malignant tumor. Rhabdomyosarcoma consists of the following four pathologic groups-embryonal, botryoid, alveolar, and pleomorphic type. While head and neck is the most common site of the embryonal rhabdomyosarcoma, the pharynx is rarely reported as a primary site of rhabdomyosarcoma. Recently, the 5-year survival rate of rhabdomyosarcoma has been greatly increased by combining therapy with radical surgery, although it still has poor prognosis. We present a case of rhabdomyosarcoma in the pharynx.